359.4 ð ç« æ«éèš Summary
359.4.1 ð äžå¥è©±çžœçµ
Liver transplant (LT) = definitive treatment for end-stage liver disease + acute liver failureïŒå°ç£ ~ 1,500-2,000 LT since program inception, living donor predominant (deceased donor shortage)ïŒindicationsïŒend-stage cirrhosis (decompensated) + ALF + HCC within Milan criteria (single †5 cm OR †3 †3 cm, no vascular/extrahepatic) + early hilar cholangiocarcinoma (Mayo protocol) + select acute alcoholic hepatitis + metabolic + HPS/POPH/FAPïŒallocationïŒMELD-Na (since 2016) or MELD 3.0 (2023) priority + exception points for HCC + HPS + POPH + FAP + CCA + cystic fibrosisïŒcontraindicationsïŒactive malignancy outside liver + severe cardiopulmonary disease + active substance abuse < 3-6 months + severe psychosocial issues + cholangiocarcinoma extrahepatic (except Mayo protocol) + active uncontrolled HIVïŒdonor typesïŒdeceased donor (DBD or DCD expanding) + living donor (right or left lobe) + split + domino (FAP) + machine perfusion (NMP, HMP â extending preservation + improving donor pool)ïŒimmunosuppression triple therapyïŒtacrolimus (CNI) + MMF + prednisone with induction (basiliximab or rATG); mTOR inhibitor (sirolimus, everolimus) for CNI nephrotoxicity / HCC recurrence preventionïŒcomplicationsïŒ(1) surgical â hepatic artery thrombosis (HAT) most serious early, biliary anastomotic stricture/leak; (2) rejection â acute cellular (pulse steroids) + antibody-mediated (plasmapheresis + IVIG + rituximab + bortezomib) + chronic ductopenia (vanishing bile duct); (3) infections â CMV (D+/R- highest, valganciclovir prophylaxis 3-12 mo) + EBV + PTLD (reduce IS + rituximab) + PCP (TMP-SMX prophylaxis) + fungal + bacterial; (4) malignancy â skin SCC + PTLD (B-cell, EBV-driven) + solid organ; (5) recurrence of disease â HCV now cured with post-LT DAAs, HBV prevented with antivirals + HBIG, PSC 30%+ recurrence, PBC 20-30%, AIH common; (6) CV (NODAT + HTN + dyslipidemia) + renal CNI nephrotoxicity (25-30% develop ESRD)ïŒoutcomesïŒ1-year 90%+, 5-year 75%, 10-year 60%; QoL generally excellentïŒspecial topicsïŒearly liver transplant for select severe alcoholic hepatitis (Mathurin 2011 + ELITAH protocols, strict psychosocial assessment); Mayo protocol for hilar cholangiocarcinoma (neoadjuvant chemoradiation + LT); acute-on-chronic liver failure (ACLF) new category â ICU + LT evaluation; machine perfusion + DCD expansion + xenotransplantation pig liver 2024 emergingã
359.4.2 ð æ²»ç粟èŠ
- immunosuppression maintenanceïŒtacrolimus (trough 8-10 early, 5-8 long-term) + MMF (1-2 g daily) + prednisone (tapered) standard triple
- inductionïŒbasiliximab (IL-2 receptor antagonist) for most + ATG (rATG / Thymoglobulin) for high-risk
- CNI nephrotoxicityïŒconsider mTOR inhibitor (sirolimus, everolimus) switch
- HCC post-LTïŒmTOR inhibitor may reduce recurrence
- CMV prophylaxisïŒvalganciclovir 3-12 months (D+/R- highest risk)
- PCP prophylaxisïŒTMP-SMX
- HBV post-LTïŒantivirals (entecavir or tenofovir) + HBIG combination â recurrence < 5%
- HCV post-LTïŒDAA treatment post-stabilization (curable)
- acute cellular rejectionïŒpulse methylprednisolone 500-1000 mg à 3 days; rATG for refractory
- antibody-mediated rejectionïŒplasmapheresis + IVIG + rituximab + bortezomib
- PTLDïŒreduce IS + rituximab (CD20+) + chemo for high-grade
359.4.3 ð¯ ç§é«åž«çèåæé
- LT indications: end-stage cirrhosis (decompensated) + ALF + HCC Milan criteria + Mayo protocol hilar CCA + select acute AH + metabolic liver disease (Wilson, hemochromatosis, alpha-1 AT)
- Milan Criteria for HCC (memorize): single †5 cm OR †3 nodules each †3 cm, no vascular invasion, no extrahepatic spread; UCSF criteria extended (†6.5 cm single or †3 each †4.5 cm total †8)
- MELD-Na (since 2016) + MELD 3.0 (2023) for allocation; MELD 3.0 adds female sex + albumin; better discrimination
- MELD exception pointsïŒHCC + HPS (hepatopulmonary) + POPH (portopulmonary HTN) + FAP + CCA (Mayo) + cystic fibrosis + polycystic liver
- donor types in Taiwan: living donor predominant (deceased donor shortage) â right lobe for adult, left for pediatric; ~ 0.5% donor mortality + 4-6 week recovery
- immunosuppression triple therapy: tacrolimus + MMF + prednisone (standard); induction basiliximab or rATG; mTOR inhibitor (sirolimus, everolimus) for CNI nephrotoxicity / HCC recurrence prevention / cardiac allograft vasculopathy
- HAT (hepatic artery thrombosis) most serious early complication: emergency revascularization or retransplant
- post-LT infection prophylaxis: valganciclovir for CMV (D+/R- highest) 3-12 months + TMP-SMX for PCP + antifungal selected + watch for EBV â PTLD
- disease recurrence post-LT: HCV now curable with DAAs, HBV prevented with antivirals + HBIG, PSC 30%+ recurrence (most), PBC 20-30%, AIH common â manage IS
- early LT for severe alcoholic hepatitis (Mathurin 2011 + ELITAH): strict psychosocial assessment + abstinence support + select cases â challenges traditional 6-month rule