348.3 🏥 內科專科考前版

348.3.1 Mechanistic Deep Dive

348.3.1.1 LES Anatomy + Function

  • Intrinsic (LES smooth muscle) + extrinsic (diaphragm crura)
  • Coordinated relaxation during swallowing
  • TLESRs occur 4-8 times per hour normally
  • Hiatal hernia impairs barrier

348.3.1.2 Pepsin in Esophagitis

  • Active at acidic pH
  • Damages esophageal mucosa
  • Causes inflammation

348.3.1.3 Barrett’s Pathogenesis

  • Chronic acid exposure → cellular changes
  • Specialized intestinal metaplasia (goblet cells with mucin)
  • CDX2 transcription factor activation
  • Progression to dysplasia → adenocarcinoma

348.3.1.4 Achalasia Pathophysiology

  • Loss of inhibitory neurons (myenteric plexus)
  • LES fails to relax
  • Absent peristalsis
  • Etiology: autoimmune, post-viral, idiopathic

348.3.2 Recent Trials & Updates

348.3.2.1 LIBERTY-EoE-TREET (2022) — Dupilumab for EoE

  • FDA approval 2022
  • ↓ Eosinophil count + symptoms
  • For ≥ 12 yo, refractory to PPI

348.3.2.2 KEYNOTE-590 (2021) — Pembrolizumab Esophageal Cancer

  • First-line for advanced esophageal
  • Both SCC + adenocarcinoma
  • ↑ OS

348.3.2.3 CheckMate 577 (2021) — Adjuvant Nivolumab

  • Post-chemoradiation/surgery for esophageal/GEJ cancer
  • ↑ DFS

348.3.2.4 Vonoprazan FDA 2022 + 2024

  • 2022: H. pylori treatment
  • 2024: erosive esophagitis

348.3.2.5 POEM Long-Term Data

  • Comparable to Heller myotomy
  • Less invasive
  • Risk of GERD post-POEM

348.3.2.6 Cendakimab + Tezepelumab for EoE

  • Phase 3 trials

348.3.3 High-Yield Specialist Points

348.3.3.1 Functional Heartburn Treatment

  • TCAs (amitriptyline)
  • SSRIs
  • Gabapentin / pregabalin
  • CBT

348.3.3.2 Reflux Hypersensitivity

  • Symptomatic without pathologic acid exposure
  • Visceral hypersensitivity
  • Pain modulators

348.3.3.3 PPI Side Effects (Long-Term)

  • B12 deficiency
  • Hypomagnesemia
  • C. diff
  • Hip fracture (debated)
  • Pneumonia (mild ↑)
  • CKD (controversial, observational)
  • Gastric polyps
  • Recommend: lowest effective dose; step-down

348.3.3.4 Anti-Reflux Surgery Selection

  • Refractory or PPI-intolerant
  • Hiatal hernia + symptoms
  • Pre-op manometry to exclude motility disorder
  • Considerations: dysphagia post-op, gas-bloat

348.3.3.5 LINX Device

  • Magnetic beads encircling LES
  • Allows swallowing + reflux barrier
  • Less side effects than Nissen
  • MRI compatibility considerations

348.3.3.6 TIF (Transoral Incisionless Fundoplication)

  • Endoscopic
  • Less invasive
  • Mixed long-term outcomes

348.3.3.7 Achalasia Type III

  • Spastic
  • POEM preferred over Heller (better outcomes for type III)

348.3.3.8 Pseudoachalasia

  • Malignancy at GEJ mimics achalasia
  • Older onset
  • Rapid weight loss
  • Workup: CT, EUS, biopsy

348.3.3.9 Esophageal Manometry

  • High-resolution manometry (HRM) standard
  • Chicago Classification 4.0 (2020)
  • Distinguishes motility disorders

348.3.3.10 Eosinophilic Esophagitis Diet

  • 6-food elimination (cow milk, wheat, egg, soy, peanut/tree nut, seafood)
  • Less restrictive 4-food or 2-food approaches
  • Add back one at a time with EGD

348.3.3.11 Barrett’s Screening Recommendations

  • High-risk: ≥ 50 yo, GERD ≥ 5 yr, male, white, central obesity, smoker, family history
  • ACG, AGA guidelines

348.3.3.12 Esophageal Cancer Lymph Node Mapping

  • Multiple levels
  • Important for staging
  • EUS-FNA

348.3.3.13 Endoscopic Therapy Stages

  • T1a (mucosal): EMR or ESD curative
  • T1b (submucosal): often requires esophagectomy (deeper invasion)
  • More advanced: multimodal

348.3.3.14 Palliation

  • Stenting for dysphagia
  • PEG tube for nutrition
  • Pain management
  • Hospice

348.3.3.15 Caustic Esophageal Injury

  • Alkali: deep penetrating
  • Acid: superficial
  • Severity assessment with endoscopy
  • Avoid gastric lavage
  • Long-term: stricture, cancer risk

348.3.4 Pearls

  • GERD: TLESRs main mechanism; PPI first-line
  • Vonoprazan (PCAB): newer; faster + more sustained acid suppression
  • Barrett’s: surveillance + RFA for dysplasia; lifelong PPI
  • EoE: dysphagia + food impaction; ≥ 15 eos/HPF; dupilumab (LIBERTY-EoE) FDA 2022
  • Achalasia: bird beak + manometry; POEM/Heller/dilation
  • Esophageal cancer: smoking + alcohol (SCC) vs GERD + Barrett’s (adeno)
  • KEYNOTE-590: pembrolizumab + chemo for esophageal cancer
  • CheckMate 577: adjuvant nivolumab