338.3 🏥 內科專科考前版

338.3.1 Mechanistic Deep Dive

338.3.1.1 T-Cell Activation

  • Signal 1: TCR + MHC + peptide
  • Signal 2: CD28 + B7 (CTLA-4 Ig blocks this — belatacept)
  • Signal 3: cytokines (IL-2, others)
  • All three needed for activation

338.3.1.2 Calcineurin Inhibitor Mechanism

  • Tacrolimus + FKBP-12 → inhibits calcineurin → ↓ NFAT → ↓ IL-2 → ↓ T-cell activation
  • Cyclosporine + cyclophilin → same downstream effect
  • Side effects: ↓ renal blood flow → CNI nephrotoxicity (afferent vasoconstriction)

338.3.1.3 MMF Mechanism

  • Inhibits inosine monophosphate dehydrogenase (IMPDH)
  • B + T cell proliferation
  • Lymphocyte-specific

338.3.1.4 mTOR Inhibitor Mechanism

  • Inhibits mTOR signaling
  • Cell cycle arrest
  • Effects on T cells, fibroblasts
  • Side effects: hyperlipidemia, edema, mouth ulcers

338.3.1.5 Belatacept Mechanism

  • Co-stimulation blockade
  • Prevents T-cell activation
  • CNI-sparing

338.3.2 Recent Trials & Updates

338.3.2.1 Xenotransplantation (Pig Kidney 2023-2024)

  • First human pig kidney transplants
  • Multiple gene edits (alpha-Gal, GHR, CMAH, etc.)
  • Limited duration
  • Future direction with iterative improvements

338.3.2.2 Tegoprubart (Anti-CD40L) Trials

  • Co-stimulation blockade
  • Phase 2 trials
  • Future alternative

338.3.2.3 Bedside Decision Algorithms

  • AI for rejection prediction
  • ctDNA + dd-cfDNA monitoring
  • Personalized immunosuppression

338.3.2.4 dd-cfDNA (Donor-Derived Cell-Free DNA)

  • AlloSure, Prospera
  • Detect rejection earlier
  • Less invasive than biopsy
  • Emerging clinical use

338.3.2.5 BENEFIT-EXT (2017, 2020) — Belatacept Long-Term

  • Better graft survival vs cyclosporine
  • Better GFR preserved
  • Higher acute rejection initially

338.3.2.6 KOLT Outcomes

  • Korean Organ Transplant data

338.3.2.7 Iscalimab (Anti-CD40)

  • Phase 2 trials
  • Co-stim blockade

338.3.3 High-Yield Specialist Points

338.3.3.1 Sensitization Management

  • Desensitization: plasmapheresis + IVIG + rituximab + sometimes proteasome inhibitor
  • IdeS (imlifidase) — single-dose
  • Approved in Europe + USA for transplant

338.3.3.2 Kidney Paired Donation (KPD)

  • Network exchanges
  • Incompatible pairs match through swaps
  • Expanded transplant access

338.3.3.3 Recurrence of FSGS Primary

  • 20-30% recurrence
  • Plasmapheresis pre-transplant (limited evidence)
  • ICZ Apheresis or RIT for severe recurrence

338.3.3.4 Anti-PLA2R + MN

  • Recurrent MN risk
  • Monitor levels
  • Anti-CD20 (rituximab) for recurrence

338.3.3.5 EBV-Negative Recipient

  • Higher PTLD risk
  • Less belatacept (EBV-naive)
  • Monitor EBV PCR
  • Prophylactic valganciclovir + acyclovir

338.3.3.6 CMV Tissue Invasive Disease

  • Treatment: ganciclovir IV 5 mg/kg q12h × 2-3 weeks → valganciclovir oral
  • Resistance: foscarnet, cidofovir, maribavir (new for refractory)
  • Letermovir prophylaxis (allotransplant primarily)

338.3.3.7 BK Virus Nephropathy

  • Plasma BK > 10,000 copies/mL
  • Renal biopsy: tubular epithelial cells with viral inclusions, T-cell infiltrate
  • Reduction of IS first-line
  • Cidofovir, IVIG for severe (limited)

338.3.3.8 Tacrolimus Drug Interactions

  • ↑ Levels: azoles (fluconazole, voriconazole), macrolides (clarithromycin), CCBs (diltiazem), grapefruit
  • ↓ Levels: rifampin, phenytoin, carbamazepine, St John’s wort
  • Therapeutic drug monitoring essential

338.3.3.9 Pregnancy After Transplant

  • Best after 1-2 years stable function
  • Cr < 1.5
  • BP controlled
  • IS adjustment: avoid MMF (teratogenic), can use azathioprine
  • Multidisciplinary management

338.3.3.10 Re-Transplant

  • For first allograft loss
  • More sensitized typically
  • Increased PRA management
  • Outcomes acceptable

338.3.3.11 Conservative Care

  • Failed transplant
  • High risk for re-transplant
  • Discussion of dialysis vs continued conservative

338.3.3.12 Living Donor Long-Term

  • Most maintain renal function
  • Small ↑ ESKD risk (long-term studies)
  • BP, kidney function follow-up
  • Pregnancy increased risk (slight)

338.3.4 Pearls

  • Transplant best for ESKD (vs dialysis)
  • LD > DD outcomes
  • Maintenance: tacrolimus + MMF + prednisone
  • Induction: basiliximab (low-risk) or rATG (high-risk)
  • Belatacept: CNI-sparing; EBV+ only
  • PTLD: EBV-driven; reduce IS + rituximab
  • CMV: valganciclovir prophylaxis 6-12 mo
  • BK nephropathy: reduce IS
  • Skin cancer: SCC > BCC
  • dd-cfDNA: emerging non-invasive marker
  • Xenotransplantation (pig kidney) 2023-2024 first human attempts