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Jones Criteria 2015 AHA Modified
- Major (CARDIAC): Carditis + Arthritis (migratory polyarthritis) + Sydenham chorea + Erythema marginatum + Subcutaneous nodules
- Minor: fever, arthralgia, â ESR/CRP, â PR interval, prior ARF
- Evidence of GAS: ASO, anti-DNase B, throat culture, scarlet fever
Subclinical Carditis (2015 Update)
- Echo evidence of valvular involvement without auscultation findings
- Now accepted in moderate/high-risk populations
Treatment
- GAS pharyngitis primary: penicillin V 10 d OR BPG IM single dose
- Acute ARF: ASA + NSAIDs (arthritis), steroids (severe carditis), bed rest, eradicate GAS
- Secondary prophylaxis: BPG IM q3-4 wk OR pen V PO BID OR erythromycin/sulfa if allergic
Secondary Prophylaxis Duration
- No carditis: 5 yr or to age 21 (whichever longer)
- Mild carditis: 10 yr or to age 21
- Severe carditis + RHD: lifelong (or age 40, varies)
Rheumatic Heart Disease
- MS most common (rheumatic = 90% globally)
- MR, AR, AS may co-exist
- PMBV (Wilkins †8) for MS
- Surgery for severe MR/AR/AS
Rheumatic Fever Mimics
- Reactive arthritis (post-infectious)
- SLE
- Lyme disease
- Endocarditis
- Juvenile idiopathic arthritis
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| Cause |
GAS pharyngitis |
S. aureus / others |
B. burgdorferi |
| Time |
2-4 wk post |
Acute |
Days-weeks post |
| Carditis |
Pancarditis |
Vegetation/abscess |
AV block |
| Treatment |
ASA/NSAID + abx |
IV abx + surgery |
Doxy/ceftriaxone |
Special Topics
Post-Strep Glomerulonephritis
- Different syndrome from ARF
- Skin infection (impetigo) or pharyngitis
- 1-2 wk post infection
- Hematuria, RBC casts, â C3
- Antibiotic doesnât prevent
Migratory vs Symmetric Polyarthritis
- ARF: migratory, asymmetric, large joints (knees, ankles, wrists)
- RA: symmetric, small joints
- Reactive arthritis: oligoarticular, asymmetric