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Sporotrichosis (âRose Gardenerâs Diseaseâ)
Pathogen
- Sporothrix schenckii complex (S. brasiliensis, S. globosa, S. luriei)
- Dimorphic fungus
- Mold in environment (soil, plants, decaying wood, rose thorns, sphagnum moss)
- Yeast in tissue
Transmission
- Traumatic inoculation through skin (rose thorn, sphagnum moss, hay bales)
- Zoonotic (cats â Brazil epidemic of cat-borne S. brasiliensis since 1998)
- Rarely inhaled / disseminated
Geography
- Worldwide, tropical + subtropical
- Brazil epidemic ongoing (cat-borne S. brasiliensis)
- USA + Latin America + Japan + Africa + Asia
- Outdoor workers, gardeners, florists
Lymphocutaneous (Most Common)
- 1-12 weeks post-inoculation
- Papulonodular lesion at inoculation site (often pruritic, may ulcerate)
- Lymphatic spread in chain along nodes (proximal to lesion)
- âSporotrichoid patternâ â multiple nodules in lymphatic chain
- Often painless
- Months without treatment
Fixed Cutaneous
- Single non-lymphatic lesion
- More chronic course
Pulmonary (Rare; Inhalation)
- COPD + immunocompromise
- Mimics TB
Disseminated (Rare)
- HIV + immunocompromise
- Skin + joints + bone + CNS
Osteoarticular
- Joint involvement
- Sometimes from disseminated
Diagnosis
- Culture of biopsy / aspirate (mold + yeast forms)
- Histology: oval / cigar-shaped yeast (less reliable than culture)
- Asteroid body (Splendore-Hoeppli reaction)
Treatment
- Itraconazole 200 mg PO bid à 3-6 months â preferred for cutaneous
- Potassium iodide (SSKI) â historic, cheap; tropical settings
- Liposomal AmB â itraconazole for severe / disseminated / pregnant
- Treat for 2-4 weeks beyond clinical resolution
Chromoblastomycosis
Pathogen
- Dematiaceous (pigmented, black) fungi: Fonsecaea pedrosoi, Cladophialophora carrionii, Phialophora verrucosa, Rhinocladiella aquaspersa
- âBlack fungiâ in tissue
Geography
- Tropical + subtropical (Latin America, Africa, Asia, parts of Australia)
- Brazil, Madagascar, Cuba, Mexico, Venezuela, Cameroon
Transmission
- Traumatic inoculation through skin (thorn, splinter, soil exposure)
- Agricultural workers + barefoot rural
Clinical
- Chronic slow-growing skin lesion (often years-decades)
- Lower extremities + arms
- Papules â nodules â verrucous (cauliflower-like) plaques + ulcers + scarring
- Often single limb / area
- Lymphatic + hematogenous spread rare (mostly localized)
Diagnosis
- Histology: âsclerotic bodies / Medlar bodies / muriform cellsâ â round brown thick-walled cells in tissue (pathognomonic)
- KOH preparation of skin scraping
- Culture (slow growth of dematiaceous mold)
Treatment
- Itraconazole + terbinafine combination à months-years
- Cryotherapy + thermotherapy adjunctive
- Surgical excision for small lesions
- Difficult to cure; long-term suppression often
Mycetoma
Background
- Chronic granulomatous infection of skin + subcutaneous tissue â bone + tissue invasion
- Triad: tumor + sinus tracts + granules
- âMadura footâ (after Madurai, India)
Eumycetoma (True Fungi)
- Madurella mycetomatis (most common)
- Madurella grisea
- Scedosporium boydii (Pseudallescheria)
- Curvularia, Acremonium, Fusarium (others)
- Black grains typically
Actinomycetoma (Filamentous Bacteria)
- Nocardia brasiliensis (most common, Latin America)
- Actinomadura madurae
- Streptomyces somaliensis (Africa)
- White, yellow, or red grains
Geography
- Tropical âMycetoma beltâ: Sudan, Senegal, India (Madurai), Mexico, Venezuela
- WHO neglected tropical disease
Clinical
- Years of slow progression
- Painless initially (foot most common)
- Progressive tumor + sinus tracts + grains
- Grain colors helpful diagnostic clue (eumycetoma vs actinomycetoma)
- Bone invasion + osteomyelitis
- Functional impairment
Diagnosis
- Grains examined microscopically + cultured
- Sclerotia (grains) color + texture
- PCR identification
- Imaging (X-ray, MRI for bone)
- Biopsy histology
Eumycetoma
- Itraconazole 400 mg/d à months-years
- Surgical resection often required
- Combination (itraconazole + terbinafine + posaconazole) some cases
Actinomycetoma
- TMP-SMX + dapsone or rifampin à months-years
- More responsive to antimicrobial than eumycetoma
- WHO MDA programs in some endemic regions